Kivonat:
Lymphangioleiomyomatosis (LAM) is a rare disease that affects women, especially in child-bearing
age. Clinical manifestations include angiomyolipoma, pneumothorax, chylothorax, cystic changes
of lungs and progressive pulmonary failure. In this article, we report a case of lung transplantation
(LuTX) for end stage pulmonary LAM and the treatment of angiomyolipoma showing growth
after LuTX resulting in complete remission with combination therapy of everolimus and tacrolimus.
Keywords
Lymphangioleiomyomatosis, Everolimus, Angiomyolipoma, Lung Transplant